Tuesday, 6 December 2016

Impaired Ribosome Biogenesis and P53 Activation in Haematological Disease: Novel Therapeutic Strategies

Modern chemotherapy of leukaemia was developed during the 1940-50s following the observation that soldiers exposed to mustard gas during World War 1 suffered from aplastic anaemia. In 1943, Louis Goodman et al. insightfully reasoned that mustard gas related compounds could inadvertently be used to treat leukaemia and lymphoma. Successful repression of lymphoma in a xenograft mouse model led to a hurried search for related chemicals with anticancer activity culminatingin the first chemotherapeutic effort to tackle childhood leukaemia in 1948,using methotrexate. 

Haematological Disease


Since then a myriad of new drugs with alternative mechanisms of action have emerged, but common to many anti-leukaemia cell toxins is their ability to induce bone marrow suppression. Aplastic anaemia (AA) is a form of bone marrow failure in which the primary defect occurs at the level of the haematological stem cell. AA is considered the paradigm of bone marrow failure syndromes and will serve as such within the context of this review. The disease is characterized by bone marrow hypocellularity, pancytopenia and is frequently associated with malignant progression. AA can be hereditary or acquired. Read more.................

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